{"id":1463,"date":"2023-08-22T08:27:11","date_gmt":"2023-08-22T08:27:11","guid":{"rendered":"https:\/\/www.insistance.org\/?p=1463"},"modified":"2023-08-22T08:27:12","modified_gmt":"2023-08-22T08:27:12","slug":"coarctation-aorte","status":"publish","type":"post","link":"https:\/\/www.insistance.org\/coarctation-aorte\/","title":{"rendered":"Coarctation de l&rsquo;aorte : une maladie cardiaque cong\u00e9nitale rare"},"content":{"rendered":"\n<p>La <strong>coarctation de l&rsquo;aorte<\/strong> est une anomalie rare du d\u00e9veloppement embryonnaire qui se caract\u00e9rise par un r\u00e9tr\u00e9cissement d&rsquo;un segment du principal vaisseau sanguin, l&rsquo;aorte. Cette maladie cardiaque cong\u00e9nitale peut avoir des cons\u00e9quences graves sur la circulation sanguine et la sant\u00e9 en g\u00e9n\u00e9ral. Dans cet article, nous aborderons les aspects cl\u00e9s concernant cette pathologie, notamment ses causes, sympt\u00f4mes, diagnostic et traitements \u00e9ventuels.<\/p>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_53 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title \" >Sommaire<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\" role=\"button\"><label for=\"item-672911d42e9fe\" ><span class=\"\"><span style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/label><input aria-label=\"Toggle\" aria-label=\"item-672911d42e9fe\"  type=\"checkbox\" id=\"item-672911d42e9fe\"><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#Anatomie_de_l%E2%80%99aorte_et_localisation_du_retrecissement\" title=\"Anatomie de l&rsquo;aorte et localisation du r\u00e9tr\u00e9cissement\">Anatomie de l&rsquo;aorte et localisation du r\u00e9tr\u00e9cissement<\/a><ul class='ez-toc-list-level-3'><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#Malformation_de_l%E2%80%99aorte_et_trouble_%C2%AB_de_G_Vaksmann_%C2%BB\" title=\"Malformation de l&rsquo;aorte et trouble \u00ab de G Vaksmann \u00bb\">Malformation de l&rsquo;aorte et trouble \u00ab de G Vaksmann \u00bb<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#La_coarctation_de_l%E2%80%99aorte_symptomes_et_complications\" title=\"La coarctation de l&rsquo;aorte : sympt\u00f4mes et complications\">La coarctation de l&rsquo;aorte : sympt\u00f4mes et complications<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#Diagnostic_antenatal_et_postnatal\" title=\"Diagnostic : ant\u00e9natal et postnatal\">Diagnostic : ant\u00e9natal et postnatal<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#Traitement_de_la_coarctation_de_l%E2%80%99aorte_chirurgie_et_dilatation_au_ballon\" title=\"Traitement de la coarctation de l&rsquo;aorte : chirurgie et dilatation au ballon\">Traitement de la coarctation de l&rsquo;aorte : chirurgie et dilatation au ballon<\/a><ul class='ez-toc-list-level-3'><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#La_chirurgie\" title=\"La chirurgie\">La chirurgie<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#La_dilatation_au_ballon_et_les_stents\" title=\"La dilatation au ballon et les stents\">La dilatation au ballon et les stents<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/#Prise_en_charge_des_recoarctations_aortiques\" title=\"Prise en charge des recoarctations aortiques\">Prise en charge des recoarctations aortiques<\/a><\/li><\/ul><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Anatomie_de_l%E2%80%99aorte_et_localisation_du_retrecissement\"><\/span>Anatomie de l&rsquo;aorte et localisation du r\u00e9tr\u00e9cissement<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>L&rsquo;<strong>aorte<\/strong> est le plus gros vaisseau sanguin qui transporte le sang oxyg\u00e9n\u00e9 depuis le c\u0153ur vers les autres organes du corps. Elle est constitu\u00e9e de plusieurs segments, dont la portion situ\u00e9e juste au-dessus de l&rsquo;\u00e9mergence de l&rsquo;art\u00e8re subclavi\u00e8re gauche est appel\u00e9e isthme aortique. C&rsquo;est pr\u00e9cis\u00e9ment \u00e0 ce niveau que se produit la coarctation, c&rsquo;est-\u00e0-dire un r\u00e9tr\u00e9cissement anormal de la lumi\u00e8re dans une section donn\u00e9e de l&rsquo;aorte.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Malformation_de_l%E2%80%99aorte_et_trouble_%C2%AB_de_G_Vaksmann_%C2%BB\"><\/span>Malformation de l&rsquo;aorte et trouble \u00ab de G Vaksmann \u00bb<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>La coarctation de l&rsquo;aorte est consid\u00e9r\u00e9e comme une malformation vasculaire rare, faisant partie des malformations cong\u00e9nitales affectant le syst\u00e8me cardiovasculaire. Elle r\u00e9sulte d&rsquo;une anomalie rare du d\u00e9veloppement embryonnaire qui provoque une r\u00e9duction de la taille de l&rsquo;aorte. Cette maladie porte \u00e9galement le nom de \u00ab trouble de G Vaksmann \u00bb, en r\u00e9f\u00e9rence au m\u00e9decin qui a d\u00e9crit pour la premi\u00e8re fois cette condition.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"La_coarctation_de_l%E2%80%99aorte_symptomes_et_complications\"><\/span>La coarctation de l&rsquo;aorte : sympt\u00f4mes et complications<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"576\" src=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7-1024x576.png\" alt=\"\" class=\"wp-image-1464\" srcset=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7-1024x576.png 1024w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7-300x169.png 300w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7-768x432.png 768w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7-1536x864.png 1536w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-7.png 1920w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\">Sch\u00e9ma du c\u0153ur et ses principales art\u00e8res<\/figcaption><\/figure>\n\n\n\n<p>Les <strong>sympt\u00f4mes<\/strong> de la coarctation de l&rsquo;aorte varient en fonction de la gravit\u00e9 du r\u00e9tr\u00e9cissement, de l&rsquo;\u00e2ge du patient et des \u00e9ventuelles autres anomalies cardiaques associ\u00e9es. Les signes cliniques les plus fr\u00e9quents sont :<\/p>\n\n\n\n<ul>\n<li>Une hypertension art\u00e9rielle<\/li>\n\n\n\n<li>Des douleurs thoraciques<\/li>\n\n\n\n<li>Un essoufflement \u00e0 l&rsquo;effort<\/li>\n\n\n\n<li>Des palpitations<\/li>\n\n\n\n<li>Des vertiges ou des \u00e9vanouissements<\/li>\n\n\n\n<li>Une fatigue excessive<\/li>\n<\/ul>\n\n\n\n<p>Ces sympt\u00f4mes peuvent \u00eatre pr\u00e9sents d\u00e8s la naissance ou appara\u00eetre progressivement avec le temps. Dans certains cas, la coarctation de l&rsquo;aorte peut \u00eatre asymptomatique et ne se manifester que lors d&rsquo;un examen m\u00e9dical de routine.<\/p>\n\n\n\n<p>Si elle n&rsquo;est pas trait\u00e9e, la coarctation de l&rsquo;aorte peut entra\u00eener diverses <strong>complications<\/strong>, telles que :<\/p>\n\n\n\n<ul>\n<li>Une insuffisance cardiaque<\/li>\n\n\n\n<li>Des troubles du rythme cardiaque<\/li>\n\n\n\n<li>Des probl\u00e8mes vasculaires, tels que des an\u00e9vrismes ou des dissections aortiques<\/li>\n\n\n\n<li>Une hypertension art\u00e9rielle r\u00e9sistante au traitement<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Diagnostic_antenatal_et_postnatal\"><\/span>Diagnostic : ant\u00e9natal et postnatal<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Le <strong>diagnostic<\/strong> de la coarctation de l&rsquo;aorte peut \u00eatre \u00e9tabli avant ou apr\u00e8s la naissance. En effet, un diagnostic ant\u00e9natal est possible gr\u00e2ce aux techniques d&rsquo;\u00e9chographie r\u00e9alis\u00e9es lors des examens pr\u00e9nataux. Dans ce cas, le m\u00e9decin peut d\u00e9tecter une anomalie dans la formation de l&rsquo;aorte et ainsi anticiper la prise en charge du nouveau-n\u00e9.<\/p>\n\n\n\n<p>Apr\u00e8s la naissance, le diagnostic repose sur plusieurs \u00e9l\u00e9ments :<\/p>\n\n\n\n<ol>\n<li>L&rsquo;examen clinique : Le m\u00e9decin cherche \u00e0 identifier les sympt\u00f4mes caract\u00e9ristiques d\u00e9crits pr\u00e9c\u00e9demment, notamment l&rsquo;hypertension art\u00e9rielle.<\/li>\n\n\n\n<li>L&rsquo;\u00e9chocardiographie : Cet examen permet d&rsquo;observer directement le r\u00e9tr\u00e9cissement aortique et d&rsquo;\u00e9valuer sa s\u00e9v\u00e9rit\u00e9.<\/li>\n\n\n\n<li>Le cath\u00e9t\u00e9risme cardiaque : Cette technique invasive consiste \u00e0 introduire un cath\u00e9ter dans les vaisseaux sanguins pour mesurer la pression art\u00e9rielle et \u00e9tudier la circulation sanguine.<\/li>\n<\/ol>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Traitement_de_la_coarctation_de_l%E2%80%99aorte_chirurgie_et_dilatation_au_ballon\"><\/span>Traitement de la coarctation de l&rsquo;aorte : chirurgie et dilatation au ballon<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"576\" src=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6-1024x576.png\" alt=\"\" class=\"wp-image-1465\" srcset=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6-1024x576.png 1024w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6-300x169.png 300w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6-768x432.png 768w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6-1536x864.png 1536w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/1-6.png 1920w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\">Op\u00e9ration chirurgicale du c\u0153ur<\/figcaption><\/figure>\n\n\n\n<p>La prise en charge de la coarctation de l&rsquo;aorte d\u00e9pend de la gravit\u00e9 du r\u00e9tr\u00e9cissement et des sympt\u00f4mes associ\u00e9s. Deux types de traitements sont g\u00e9n\u00e9ralement envisag\u00e9s :<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"La_chirurgie\"><\/span>La chirurgie<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Le traitement chirurgical consiste \u00e0 retirer la portion r\u00e9tr\u00e9cie de l&rsquo;aorte et \u00e0 reconnecter les deux extr\u00e9mit\u00e9s saines. Cette intervention est g\u00e9n\u00e9ralement r\u00e9alis\u00e9e chez les nouveau-n\u00e9s et les jeunes enfants pr\u00e9sentant une coarctation s\u00e9v\u00e8re.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"La_dilatation_au_ballon_et_les_stents\"><\/span>La dilatation au ballon et les stents<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Pour les patients plus \u00e2g\u00e9s ou ceux qui pr\u00e9sentent un risque chirurgical \u00e9lev\u00e9, une alternative moins invasive peut \u00eatre propos\u00e9e : la <strong>dilatation au ballon<\/strong>. Ce traitement consiste \u00e0 introduire un cath\u00e9ter muni d&rsquo;un ballon gonflable dans l&rsquo;aorte r\u00e9tr\u00e9cie, puis \u00e0 gonfler progressivement le ballon pour \u00e9largir la lumi\u00e8re aortique. Dans certains cas, un dispositif m\u00e9tallique appel\u00e9 stent peut \u00eatre plac\u00e9 pour maintenir l&rsquo;ouverture de l&rsquo;aorte.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Prise_en_charge_des_recoarctations_aortiques\"><\/span>Prise en charge des recoarctations aortiques<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Dans certains cas, la coarctation de l&rsquo;aorte peut r\u00e9appara\u00eetre apr\u00e8s un traitement initial, ce qui est appel\u00e9 une <strong>recoarctation aortique<\/strong>. Le choix du traitement d\u00e9pend des caract\u00e9ristiques du patient et de la gravit\u00e9 de la r\u00e9cidive. La dilatation au ballon et la pose de stents sont souvent utilis\u00e9es comme traitement des obstructions r\u00e9currentes.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>La coarctation de l&rsquo;aorte est une anomalie rare du d\u00e9veloppement embryonnaire qui se caract\u00e9rise par un r\u00e9tr\u00e9cissement d&rsquo;un segment du principal vaisseau sanguin, l&rsquo;aorte. Cette&#46;&#46;&#46;<\/p>\n","protected":false},"author":5,"featured_media":1466,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[51],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v21.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Coarctation de l&#039;aorte : une maladie cardiaque cong\u00e9nitale rare - Insistance.org<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.insistance.org\/coarctation-aorte\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Coarctation de l&#039;aorte : une maladie cardiaque cong\u00e9nitale rare - Insistance.org\" \/>\n<meta property=\"og:description\" content=\"La coarctation de l&rsquo;aorte est une anomalie rare du d\u00e9veloppement embryonnaire qui se caract\u00e9rise par un r\u00e9tr\u00e9cissement d&rsquo;un segment du principal vaisseau sanguin, l&rsquo;aorte. 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Ceci ne fait pas foi d&#039;avis m\u00e9dical. 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