{"id":1478,"date":"2023-08-22T08:58:28","date_gmt":"2023-08-22T08:58:28","guid":{"rendered":"https:\/\/www.insistance.org\/?p=1478"},"modified":"2023-08-23T13:57:30","modified_gmt":"2023-08-23T13:57:30","slug":"syringomyelie","status":"publish","type":"post","link":"https:\/\/www.insistance.org\/syringomyelie\/","title":{"rendered":"Comprendre la syringomy\u00e9lie : sympt\u00f4mes, causes et traitements"},"content":{"rendered":"\n<p>La <strong>syringomy\u00e9lie<\/strong> est une maladie rare qui affecte la moelle \u00e9pini\u00e8re. Elle se caract\u00e9rise par la formation de cavit\u00e9s remplies de liquide c\u00e9phalo-rachidien \u00e0 l&rsquo;int\u00e9rieur de la moelle. Dans cet article, nous allons explorer les causes, les sympt\u00f4mes et les diff\u00e9rentes options de traitement disponibles pour cette affection.<\/p>\n\n\n\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_53 counter-hierarchy ez-toc-counter ez-toc-grey ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title \" >Sommaire<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\" role=\"button\"><label for=\"item-672911cc9850b\" ><span class=\"\"><span style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/label><input aria-label=\"Toggle\" aria-label=\"item-672911cc9850b\"  type=\"checkbox\" id=\"item-672911cc9850b\"><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Symptomes_et_manifestations_de_la_syringomyelie\" title=\"Sympt\u00f4mes et manifestations de la syringomy\u00e9lie\">Sympt\u00f4mes et manifestations de la syringomy\u00e9lie<\/a><ul class='ez-toc-list-level-3'><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Autres_manifestations_possibles\" title=\"Autres manifestations possibles\">Autres manifestations possibles<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Causes_de_la_syringomyelie\" title=\"Causes de la syringomy\u00e9lie\">Causes de la syringomy\u00e9lie<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Options_de_traitement_pour_la_syringomyelie\" title=\"Options de traitement pour la syringomy\u00e9lie\">Options de traitement pour la syringomy\u00e9lie<\/a><ul class='ez-toc-list-level-3'><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Gestion_des_symptomes\" title=\"Gestion des sympt\u00f4mes\">Gestion des sympt\u00f4mes<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.insistance.org\/syringomyelie\/#Traitements_chirurgicaux\" title=\"Traitements chirurgicaux\">Traitements chirurgicaux<\/a><\/li><\/ul><\/li><\/ul><\/nav><\/div>\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Symptomes_et_manifestations_de_la_syringomyelie\"><\/span>Sympt\u00f4mes et manifestations de la syringomy\u00e9lie<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"576\" src=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10-1024x576.png\" alt=\"\" class=\"wp-image-1479\" srcset=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10-1024x576.png 1024w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10-300x169.png 300w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10-768x432.png 768w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10-1536x864.png 1536w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/2-10.png 1920w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\"><em>Sch\u00e9ma de la moelle \u00e9pini\u00e8re<\/em><\/figcaption><\/figure><\/div>\n\n\n<p>Les sympt\u00f4mes de la syringomy\u00e9lie varient en fonction de l&#8217;emplacement et de la taille des cavit\u00e9s dans la moelle \u00e9pini\u00e8re. Les signes peuvent \u00eatre progressifs et appara\u00eetre lentement, ou ils peuvent survenir soudainement en raison d&rsquo;une blessure ou d&rsquo;un stress. Les sympt\u00f4mes communs incluent :<\/p>\n\n\n\n<ul>\n<li><strong>Douleur<\/strong> &#8211; La douleur peut \u00eatre ressentie dans le dos, les \u00e9paules, les bras ou les jambes. Elle peut \u00eatre sourde, aigu\u00eb ou br\u00fblante.<\/li>\n\n\n\n<li><strong>Faiblesse musculaire<\/strong> &#8211; Une faiblesse dans les muscles des membres sup\u00e9rieurs ou inf\u00e9rieurs peut survenir, rendant difficile la r\u00e9alisation de certaines t\u00e2ches quotidiennes.<\/li>\n\n\n\n<li><strong>Perte de sensibilit\u00e9<\/strong> &#8211; Certaines personnes atteintes de syringomy\u00e9lie peuvent perdre la capacit\u00e9 de sentir la temp\u00e9rature ou la douleur sur certaines parties de leur corps.<\/li>\n\n\n\n<li><strong>Probl\u00e8mes de coordination<\/strong> &#8211; Des probl\u00e8mes pour coordonner les mouvements des mains et des pieds peuvent survenir, rendant difficile la marche ou la r\u00e9alisation de t\u00e2ches manuelles.<\/li>\n\n\n\n<li><strong>Difficult\u00e9s \u00e0 uriner et \u00e0 contr\u00f4ler les intestins<\/strong> &#8211; Certains patients peuvent \u00e9prouver des probl\u00e8mes pour vider leur vessie ou contr\u00f4ler leurs intestins.<\/li>\n<\/ul>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Autres_manifestations_possibles\"><\/span>Autres manifestations possibles<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>D&rsquo;autres sympt\u00f4mes moins communs mais potentiellement graves peuvent \u00e9galement \u00eatre associ\u00e9s \u00e0 la syringomy\u00e9lie. Ceux-ci incluent :<\/p>\n\n\n\n<ul>\n<li><strong>Scoliose<\/strong> &#8211; La formation d&rsquo;une courbe anormale de la colonne vert\u00e9brale peut r\u00e9sulter de la maladie.<\/li>\n\n\n\n<li><strong>Difficult\u00e9s respiratoires<\/strong> &#8211; Dans certains cas, les probl\u00e8mes respiratoires peuvent survenir en raison de l&rsquo;impact de la maladie sur les muscles qui aident \u00e0 la respiration.<\/li>\n\n\n\n<li><strong>Paralysie<\/strong> &#8211; Dans les cas extr\u00eames, la syringomy\u00e9lie peut provoquer une paralysie partielle ou totale des membres.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Causes_de_la_syringomyelie\"><\/span>Causes de la syringomy\u00e9lie<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>La cause exacte de la syringomy\u00e9lie n&rsquo;est pas encore enti\u00e8rement comprise. Cependant, nous savons aujourd&rsquo;hui que certains facteurs contribuent au d\u00e9veloppement de cette maladie. Les causes possibles incluent :<\/p>\n\n\n\n<ul>\n<li><a href=\"https:\/\/www.insistance.org\/malformation-chiari\/\" target=\"_blank\" rel=\"noreferrer noopener\">Malformation de Chiari<\/a> &#8211; Cette malformation cong\u00e9nitale entra\u00eene un positionnement anormal du cervelet, ce qui peut provoquer une pression sur la moelle \u00e9pini\u00e8re et favoriser le d\u00e9veloppement de cavit\u00e9s.<\/li>\n\n\n\n<li><strong>Traumatismes<\/strong> &#8211; Des blessures \u00e0 la colonne vert\u00e9brale ou \u00e0 la moelle \u00e9pini\u00e8re peuvent endommager les tissus et provoquer la formation de cavit\u00e9s.<\/li>\n\n\n\n<li><strong>M\u00e9ningite<\/strong> &#8211; Les infections du syst\u00e8me nerveux central, comme la m\u00e9ningite, peuvent provoquer des inflammations qui entra\u00eenent la formation de cavit\u00e9s dans la moelle \u00e9pini\u00e8re.<\/li>\n\n\n\n<li><strong>Tumeurs<\/strong> &#8211; La pr\u00e9sence de tumeurs dans la r\u00e9gion de la moelle \u00e9pini\u00e8re peut provoquer un d\u00e9placement du liquide c\u00e9phalo-rachidien et la formation de cavit\u00e9s.<\/li>\n\n\n\n<li><strong>Anomalies vasculaires<\/strong> &#8211; Les anomalies des vaisseaux sanguins autour de la moelle \u00e9pini\u00e8re peuvent perturber la circulation du liquide c\u00e9phalo-rachidien et contribuer au d\u00e9veloppement de la syringomy\u00e9lie.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Options_de_traitement_pour_la_syringomyelie\"><\/span>Options de traitement pour la syringomy\u00e9lie<span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img decoding=\"async\" loading=\"lazy\" width=\"1024\" height=\"576\" src=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8-1024x576.png\" alt=\"\" class=\"wp-image-1480\" srcset=\"https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8-1024x576.png 1024w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8-300x169.png 300w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8-768x432.png 768w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8-1536x864.png 1536w, https:\/\/www.insistance.org\/wp-content\/uploads\/2023\/08\/3-8.png 1920w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\"><em>Cette maladie engendre d&rsquo;intenses douleurs <\/em><\/figcaption><\/figure><\/div>\n\n\n<p>Le traitement de la syringomy\u00e9lie d\u00e9pend de la cause sous-jacente ainsi que de la gravit\u00e9 des sympt\u00f4mes. Dans certains cas, des interventions m\u00e9dicales ou chirurgicales peuvent \u00eatre n\u00e9cessaires pour traiter la cause et soulager les sympt\u00f4mes. Les options de traitement incluent :<\/p>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Gestion_des_symptomes\"><\/span>Gestion des sympt\u00f4mes<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>La gestion des sympt\u00f4mes est souvent la premi\u00e8re \u00e9tape du traitement pour les personnes atteintes de syringomy\u00e9lie. Cela peut inclure :<\/p>\n\n\n\n<ul>\n<li><strong>M\u00e9dicaments<\/strong> &#8211; Des m\u00e9dicaments anti-inflammatoires non st\u00e9ro\u00efdiens (AINS) ou des analg\u00e9siques peuvent \u00eatre prescrits pour g\u00e9rer la douleur et l&rsquo;inflammation.<\/li>\n\n\n\n<li><strong>Physioth\u00e9rapie<\/strong> &#8211; Un programme de physioth\u00e9rapie individualis\u00e9 peut aider \u00e0 renforcer les muscles, am\u00e9liorer la coordination et la mobilit\u00e9, et soulager certains sympt\u00f4mes de la maladie.<\/li>\n\n\n\n<li><strong>Orth\u00e8ses<\/strong> &#8211; Des dispositifs orthop\u00e9diques tels que des attelles ou des corsets peuvent \u00eatre utilis\u00e9s pour aider \u00e0 soutenir les membres affect\u00e9s par la faiblesse musculaire ou la perte de sensibilit\u00e9.<\/li>\n<\/ul>\n\n\n\n<h3 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Traitements_chirurgicaux\"><\/span>Traitements chirurgicaux<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Dans certains cas, une intervention chirurgicale peut \u00eatre n\u00e9cessaire pour traiter la cause sous-jacente de la syringomy\u00e9lie ou pour soulager la pression sur la moelle \u00e9pini\u00e8re. Les options chirurgicales incluent :<\/p>\n\n\n\n<ul>\n<li><strong>Intervention pour les malformations de Chiari<\/strong> &#8211; Une d\u00e9compression de la fosse post\u00e9rieure peut \u00eatre r\u00e9alis\u00e9e pour cr\u00e9er plus d&rsquo;espace pour le cervelet et r\u00e9duire la pression sur la moelle \u00e9pini\u00e8re.<\/li>\n\n\n\n<li><strong>Drainage des cavit\u00e9s<\/strong> &#8211; Un shunt peut \u00eatre ins\u00e9r\u00e9 pour drainer le liquide c\u00e9phalo-rachidien des cavit\u00e9s et soulager la pression sur la moelle \u00e9pini\u00e8re.<\/li>\n\n\n\n<li><strong>Abord chirurgical des tumeurs<\/strong> &#8211; Dans les cas o\u00f9 une tumeur est \u00e0 l&rsquo;origine de la syringomy\u00e9lie, une intervention peut \u00eatre n\u00e9cessaire pour enlever la tumeur ou r\u00e9duire sa taille.<\/li>\n<\/ul>\n\n\n\n<p>La syringomy\u00e9lie est une maladie complexe qui n\u00e9cessite souvent une approche multidisciplinaire pour le diagnostic et le traitement. Les m\u00e9decins, les neurologues, les orthop\u00e9distes et les physioth\u00e9rapeutes travaillent souvent ensemble pour fournir un plan de traitement complet et adapt\u00e9 aux besoins individuels des patients.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>La syringomy\u00e9lie est une maladie rare qui affecte la moelle \u00e9pini\u00e8re. Elle se caract\u00e9rise par la formation de cavit\u00e9s remplies de liquide c\u00e9phalo-rachidien \u00e0 l&rsquo;int\u00e9rieur&#46;&#46;&#46;<\/p>\n","protected":false},"author":5,"featured_media":1481,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[51],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v21.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Comprendre la syringomy\u00e9lie : sympt\u00f4mes, causes et traitements - Insistance.org<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.insistance.org\/syringomyelie\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Comprendre la syringomy\u00e9lie : sympt\u00f4mes, causes et traitements - Insistance.org\" \/>\n<meta property=\"og:description\" content=\"La syringomy\u00e9lie est une maladie rare qui affecte la moelle \u00e9pini\u00e8re. 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